| CASE REPORT |
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| Year : 2017 | Volume
: 3
| Issue : 2 | Page : 280-284 |
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Primary intramural fibromatosis of the small bowel: An uncommon cause of intestinal obstruction
Maggie J Lin1, Richard P Sharpe1, Stanislaw P Stawicki2, Santo Longo3, Lisa Stoll3
1 Department of Surgery, St. Luke's University Health Network, Bethlehem, Pennsylvania, USA
2 Department of Research and Innovation, St. Luke's University Health Network, Bethlehem, Pennsylvania, USA
3 Department of Pathology, St. Luke's University Health Network, Bethlehem, Pennsylvania, USA
Correspondence Address:
Dr. Stanislaw P Stawicki
Department of Research and Innovation, St. Luke's University Health Network, EW2 Research Administration, 801 Ostrum Street, Bethlehem, Pennsylvania 18015
USA
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/2455-5568.222474
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Small bowel obstruction is a commonly encountered surgical diagnosis, most frequently attributed to hernias, adhesions, or malignancy. Intra-abdominal fibromatoses are rare tumors with heterogeneous clinical manifestations. Infrequently, acute presentation of bowel obstruction may be associated with intra-abdominal fibromatosis – also referred to as “desmoid tumor” – a benign proliferation of myofibroblasts which most often arise from the mesentery or retroperitoneum and are nonmalignant in character. Here, we describe a case of an isolated abdominal fibromatosis with primary involvement of the intestinal wall and the clinical presentation of bowel obstruction. The patient was managed by surgical resection and had complete recovery. As demonstrated in the current case, physically small, relatively isolated desmoid tumors have the potential to significantly impact the patient. Individualized treatment approaches produce good clinical outcomes in most cases.
The following core competencies are addressed in this article: Medical knowledge, Patient care.
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